Myxoid Chondrosarcoma of the Sinonasal Cavity in a Child: a Case Report
Korean Journal of Radiology
;
: 452-455, 2007.
Artículo
en Inglés
| WPRIM
| ID: wpr-227239
ABSTRACT
Chondrosarcomas are malignant tumors of cartilage that rarely involve the sinonasal region, and myxoid chondrosarcoma is a rare histologic variant of chondrosarcoma that usually occurs in the soft tissue of extremities. Although several case reports and results of small series of chondrosarcomas in the sinonasal region in children are available, myxoid type chondrosarcoma is extremely rare. We recently experienced a case of low grade myxoid chondrosarcoma involving the sinonasal cavity in a 10-year-old boy, and here we report its radiologic-pathologic findings. In this case, chondroid calcification on CT and septal and marginal enhancement on MRI suggested a chondrosarcoma. Whole body PET-CT demonstrated no definite metastatic lesion and a low peak standardized uptake value primary tumor. However, no definite distinguishing imaging features were observed that distinguished low grade myxoid chondrosarcoma from conventional chondrosarcoma.
Texto completo:
Disponible
Índice:
WPRIM (Pacífico Occidental)
Asunto principal:
Senos Paranasales
/
Neoplasias Óseas
/
Imagen por Resonancia Magnética
/
Tomografía Computarizada por Rayos X
/
Estudios de Seguimiento
/
Condrosarcoma
/
Enfermedades Raras
/
Tomografía de Emisión de Positrones
/
Diagnóstico Diferencial
/
Imagen de Cuerpo Entero
Tipo de estudio:
Estudio diagnóstico
/
Estudio observacional
/
Estudio pronóstico
Límite:
Niño
/
Humanos
/
Masculino
Idioma:
Inglés
Revista:
Korean Journal of Radiology
Año:
2007
Tipo del documento:
Artículo
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