Dandy-Walker complex: a clinicopathologic study of 9 cases / 中华病理学杂志
Chinese Journal of Pathology
;
(12): 815-818, 2013.
Artículo
en Chino
| WPRIM
| ID: wpr-288200
ABSTRACT
<p><b>OBJECTIVE</b>To investigate the etiology, pathogenesis, clinicopathologic characteristics, clinical prognosis and treatment of Dandy-Walker syndrome.</p><p><b>METHODS</b>Nine cases of Dandy-Walker syndrome were included in the study. The autopsy findings and clinical history were evaluated along with review of the literature. The causes, pathogenetic mechanism, pathologic features and prognosis of Dandy-Walker syndrome were analyzed.</p><p><b>RESULTS</b>Among 9 Dandy-Walker syndrome cases, six patients presented with variants of Dandy-Walker complex and 3 cases had classic Dandy-Walker malformation. In addition, 4 patients presented with combined lateral ventricle expansion and multiple malformations were seen in 7 cases. Combined umbilical cord abnormality was noted in 4 patients with variant of Dandy-Walker complex and combined placental abnormality was seen in one classic Dandy-Walker syndrome.</p><p><b>CONCLUSIONS</b>Dandy-Walker syndrome is a rare disease. In addition to complex pathogenesis with possible genetic and environmental antigenic etiologies, placental and umbilical cord abnormality may be also related to its development.</p>
Texto completo:
Disponible
Índice:
WPRIM (Pacífico Occidental)
Asunto principal:
Patología
/
Insuficiencia Placentaria
/
Autopsia
/
Diagnóstico por Imagen
/
Estudios Retrospectivos
/
Ultrasonografía Prenatal
/
Edad Gestacional
/
Aborto Inducido
/
Ventrículos Laterales
/
Síndrome de Dandy-Walker
Tipo de estudio:
Estudio diagnóstico
/
Estudio observacional
/
Estudio pronóstico
Límite:
Femenino
/
Humanos
/
Masculino
/
Embarazo
Idioma:
Chino
Revista:
Chinese Journal of Pathology
Año:
2013
Tipo del documento:
Artículo
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