New insight into pathogenesis of idiopathic myelofibrosis--review / 中国实验血液学杂志
Journal of Experimental Hematology
;
(6): 1330-1334, 2007.
Artículo
en Chino
| WPRIM
| ID: wpr-318729
ABSTRACT
Idiopathic myelofibrosis is a type of chronic myeloproliferative disorders characterized by splenomegaly, a leukoerythroblastic blood picture, teardrop poikilocytosis, in various degrees of bone marrow fibrosis and extramedullary hematopoiesis. In this paper, the biological characters and pathogenesis of idiopathic myelofibrosis such as mutation of tyrosine kinase receptor, mutation of GABA transporter 1, JAK2 mutation and c-MPl mutation, as well as other pathogenesis related with idiopathic myelofibrosis were reviewed.
Texto completo:
Disponible
Índice:
WPRIM (Pacífico Occidental)
Asunto principal:
Proteínas Tirosina Quinasas Receptoras
/
Proteínas Transportadoras de GABA en la Membrana Plasmática
/
Janus Quinasa 2
/
Receptores de Trombopoyetina
/
Mielofibrosis Primaria
/
Genética
/
Mutación
Tipo de estudio:
Estudio de etiología
Límite:
Humanos
Idioma:
Chino
Revista:
Journal of Experimental Hematology
Año:
2007
Tipo del documento:
Artículo
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