Primary pulmonary sarcoma-a study of 8 cases / 中国医学科学院学报

ABSTRACT

<p><b>OBJECTIVE</b>To summarize the diagnosis, pathology, treatment and prognosis of 8 cases of primary pulmonary sarcoma.</p><p><b>METHOD</b>The clinical data of 8 patients with primary pulmonary sarcoma in the PUMC Hospital from 1986 to 2009 were retrospectively analyzed.</p><p><b>RESULTS</b>The clinical manifestations included cough (n=5), chest pain (n=2), hemoptysis (n=2), short of breath (n=2), and hoarseness due to the oppression of the recurrent laryngeal nerve (n=1). The pathological diagnoses included leiomyosarcoma (n=1), synovial sarcoma (n=1), malignant fibrous histiocytoma (n=1), and unknown tumors due to poor differentiation (n=5). The 1- and 5-year survival rate was 37.5 % and 12.5%, respectively.</p><p><b>CONCLUSIONS</b>The primary pulmonary sarcoma is a rare disease with non-specific clinical manifestations. The early diagnosis is difficult and the prognosis is poor. Currently no satisfactory therapy is available for this disease.</p>