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Nodal marginal zone B-cell lymphoma: a clinicopathologic study of 10 cases / 中华病理学杂志
Chinese Journal of Pathology ; (12): 529-533, 2007.
Artículo en Chino | WPRIM | ID: wpr-347740
ABSTRACT
<p><b>OBJECTIVE</b>To study the morphologic features, immunophenotype, differential diagnosis and prognosis of nodal marginal zone B-cell lymphoma (NMZL).</p><p><b>METHODS</b>Light microscopic examination and immunohistochemical study were carried out in 10 cases of NMZL. Seven of which had follow-up information available.</p><p><b>RESULTS</b>All cases presented with good performance status at the time of diagnosis. Amongst the 7 cases with follow-up information available, most (6/7) were in advanced clinical stage (stage II to III). The one-year survival rate was 67%. A vaguely nodular growth pattern was observed in most cases of NMZL (5/10). The lymphoma was composed predominantly of atypical lymphoid cells resembling centrocytes (7/10). A predominance of monocytoid B-cell (2/10) or small lymphocytic (1/10) morphology was rare. Instead, the presence of a minor component of monocytoid B cells was not uncommon (5/10). Plasmacytoid or plasmacytic cells were also frequently found (8/10). The proliferation index ranged from 5% to 50%. Follicular dendritic cells appeared atrophic in 7 cases and variably hyperplasic in 3 cases.</p><p><b>CONCLUSIONS</b>Primary NMZL is rare. It has a unique growth pattern and most cases are composed predominantly of cells resembling centrocytes. Differential diagnosis includes lymphoplasmacytic lymphoma, lymph node involvement by extranodal marginal zone B-cell lymphoma and T-zone hyperplasia. The clinical stage is often high at presentation, with systemic dissemination. The prognosis of NMZL is thus relatively poor.</p>
Asunto(s)
Texto completo: Disponible Índice: WPRIM (Pacífico Occidental) Asunto principal: Patología / Inducción de Remisión / Tasa de Supervivencia / Estudios de Seguimiento / Macroglobulinemia de Waldenström / Linfoma de Células B de la Zona Marginal / Proteínas Proto-Oncogénicas c-bcl-2 / Diagnóstico Diferencial / Quimioterapia / Ganglios Linfáticos Tipo de estudio: Estudio diagnóstico / Estudio observacional / Estudio pronóstico Límite: Adulto / Anciano / Femenino / Humanos / Masculino Idioma: Chino Revista: Chinese Journal of Pathology Año: 2007 Tipo del documento: Artículo

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Texto completo: Disponible Índice: WPRIM (Pacífico Occidental) Asunto principal: Patología / Inducción de Remisión / Tasa de Supervivencia / Estudios de Seguimiento / Macroglobulinemia de Waldenström / Linfoma de Células B de la Zona Marginal / Proteínas Proto-Oncogénicas c-bcl-2 / Diagnóstico Diferencial / Quimioterapia / Ganglios Linfáticos Tipo de estudio: Estudio diagnóstico / Estudio observacional / Estudio pronóstico Límite: Adulto / Anciano / Femenino / Humanos / Masculino Idioma: Chino Revista: Chinese Journal of Pathology Año: 2007 Tipo del documento: Artículo