A Case of Eosinophilic Granulomatosis with Polyangiitis Presenting with Subarachnoid Hemorrhage and Mononeuritis Multiplex
Journal of Rheumatic Diseases
;
: 190-194, 2015.
Artículo
en Coreano
| WPRIM
| ID: wpr-36842
ABSTRACT
Eosinophilic granulomatosis with polyangiitis (EGPA), previously called Churg-Strauss syndrome, is an anti-neutrophil cytoplasmic antibody associated vasculitis, accompanied by asthma, hypereosinophilia, nonfixed pulmonary infiltrates, and sinusitis. Peripheral neuropathy is common in patients with EGPA; however, a few cases of EGPA with central nervous system (CNS) involvement have been reported. A 45-year-old female referred for right side weakness and posterior neck pain was diagnosed as EGPA with subarachnoid hemorrhage and mononeuritis multiplex. She was effectively treated with a high dose glucocorticoid, cyclophosphamide, and intravenous immunoglobulin. EGPA with CNS involvement is uncommon and causes significant morbidity and mortality. Therefore more rapid and accurate diagnostic evaluation may be required. EGPA should be considered in patients with neurological symptoms and hypereosinophilia.
Texto completo:
Disponible
Índice:
WPRIM (Pacífico Occidental)
Asunto principal:
Asma
/
Sinusitis
/
Hemorragia Subaracnoidea
/
Vasculitis
/
Inmunoglobulinas
/
Síndrome de Churg-Strauss
/
Sistema Nervioso Central
/
Mortalidad
/
Enfermedades del Sistema Nervioso Periférico
/
Dolor de Cuello
Tipo de estudio:
Estudio pronóstico
Límite:
Femenino
/
Humanos
Idioma:
Coreano
Revista:
Journal of Rheumatic Diseases
Año:
2015
Tipo del documento:
Artículo
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