Atypical Teratoid Rhabdoid Tumors in Adult Patient with Multiple Lesions

ABSTRACT

Primary atypical teratoid/rhabdoid tumor(AT/RT) of the central nervous system is a recently described, highly malignant neoplasm that usually occur in the posterior fossa of children. Although AT/RT usually occurs in young children, AT/RT is being recognized in adults with increasing frequency. The authors report 49-year-old man with multiple AT/RT lesions (right lateral ventricle, right temporal lobe and right cerebellum). Histopathologic findings showed typical rhabdoid cells with eccentric nuclei and prominent nucleoli. Eventhough the tumor was removed, a patient was dead in one month after surgery due to recurrence and rapid regrowth of the tumor.