Focal Segmental Glomerulosclerosis in a Child with Prader-Willi Syndrome: A Case of Obesity-associated Focal Segmental Glomerulosclerosis
Journal of the Korean Society of Pediatric Nephrology
;
: 244-249, 2004.
Artículo
en Inglés
| WPRIM
| ID: wpr-46790
ABSTRACT
Obesity-associated focal segmental glomerulosclerosis(OB-FSGS) has been known to progress into advanced renal insufficiency, and its clinicopathological features include obesity, FSGS lesions with glomerulomegaly and, nephrotic-range proteinuria without edema. A 14- year old girl with Prader-Willi syndrome showed nephrotic-range proteinuria without hypoalbuminemia or edema. The renal biopsy revealed focal segmental glomerulosclerosis together with glomerular hypertrophy and an increased mesangial matrix. We report here a case of OB-FSGS as one of the renal problems of Prader-Willi syndrome, and we came to the conclusion that Prader-Willi syndrome is one of the possible disease entities that can lead to renal insufficiency through obesity.
Texto completo:
Disponible
Índice:
WPRIM (Pacífico Occidental)
Asunto principal:
Síndrome de Prader-Willi
/
Proteinuria
/
Biopsia
/
Glomeruloesclerosis Focal y Segmentaria
/
Hipoalbuminemia
/
Edema
/
Insuficiencia Renal
/
Hipertrofia
/
Obesidad
Límite:
Niño
/
Femenino
/
Humanos
Idioma:
Inglés
Revista:
Journal of the Korean Society of Pediatric Nephrology
Año:
2004
Tipo del documento:
Artículo
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