Advances in primary systemic anaplastic large cell lymphoma / 白血病·淋巴瘤

ABSTRACT

Primary systemic anaplastic large cell lymphoma is a subtype of rare and heterogeneous clinical entity.There is no standard treatment as yet.Based on retrospective studies,systematic chemotherapy is the main treatment while combining field radiation with chemotherapy is always used for diseases at early stage. Recently, there are some improvement were made on this kind of disease in the pathology and pathogenesis because of the advancement in molecular biology. This review focuses on the pathogenesis,pathology,treatment and prognosis of primary systemic anaplastic large cell lymphoma.