A Case of Rudimentary Meningocele / 대한피부과학회지

ABSTRACT

Rudimentary meningocele, also known as a 'variant of primary cutaneous meningioma' or 'acoelic meningeal hamartoma', is an unusual developmental anomaly in which meningothelial elements are found in the skin. A 8-month-old girl has a well-circumscribed, alopecic, atrophic patch on the midline of the occipital area since birth. Histologically, pseudovascular spaces lined with flattened or cuboidal cells were seen in the papillary and upper reticular dermis without collagen bodies. These flattened or cuboidal cells were positive for vimentin, but negative for EMA, immunohistochemically. Radiographic finding of the scalp revealed no underlying bony defect.