A Case of Multiple Endocrine Neoplasia type 3 With Multiple Mucosal Neuroma / 대한피부과학회지
Korean Journal of Dermatology
;
: 505-509, 1999.
Artículo
en Coreano
| WPRIM
| ID: wpr-52584
ABSTRACT
Multiple endocrine neoplasi~a type 3 is a rare, heritable or sporadic, multiple neoplastic disorder that is charracterized by thyroid medullary careinoma, pheochromocytoma, multiple mucosal neuroma, and marfanoid habitus. The most important disorder of the syndrome is mucosal neuroma that is an early diagnostic sign of multiple endocrine neoplasia type 3. Early diagnosis of MEN type 3 determines prognosis of the disease. We present a case of multiple endocrine neoplasia type 3 of the sporadic pattern in a 27-year-old man who had typical medullary thyroid carcinoma, mucosal neuroma, marfanoid habitus, and megacolon.
Texto completo:
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Índice:
WPRIM (Pacífico Occidental)
Asunto principal:
Feocromocitoma
/
Pronóstico
/
Glándula Tiroides
/
Neoplasia Endocrina Múltiple
/
Neoplasias de la Tiroides
/
Diagnóstico Precoz
/
Megacolon
/
Neuroma
Tipo de estudio:
Estudio diagnóstico
/
Estudio pronóstico
/
Estudio de tamizaje
Límite:
Adulto
/
Humanos
/
Masculino
Idioma:
Coreano
Revista:
Korean Journal of Dermatology
Año:
1999
Tipo del documento:
Artículo
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