A Case of Glanzmann's Thrombasthenia Successfully Managed after Tonsillectomy / 임상소아혈액종양
Clinical Pediatric Hematology-Oncology
;
: 29-32, 2014.
Artículo
en Inglés
| WPRIM
| ID: wpr-53107
ABSTRACT
Glanzmann's thrombasthenia (GT) is a rare autosomal recessive disease and platelet function disorder, in which platelet membrane GP IIb/ IIIa complex is defective and platelet aggregation is undeveloped. GT is characterized by mucocutaneous hemorrhages, such as, epistaxis, purpura, gingival bleeding, and menorrhagia, severe bleeding complications during surgery. We report the case of a 6-year-old boy with GT who underwent tonsillectomy. Here, we focus on perioperative hemostatic management using recombinant factor VIIa, fibrin glue and hemostat materials.
Texto completo:
Disponible
Índice:
WPRIM (Pacífico Occidental)
Asunto principal:
Púrpura
/
Tonsilectomía
/
Plaquetas
/
Trombastenia
/
Factor VIIa
/
Adhesivo de Tejido de Fibrina
/
Agregación Plaquetaria
/
Epistaxis
/
Hemorragia
/
Hemostasis
Límite:
Niño
/
Femenino
/
Humanos
/
Masculino
Idioma:
Inglés
Revista:
Clinical Pediatric Hematology-Oncology
Año:
2014
Tipo del documento:
Artículo
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