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Pulmonary Hypertension in Patient with Neurofibromatosis Type 1 / 고신대학교의과대학학술지
Kosin Medical Journal ; : 227-232, 2017.
Artículo en Inglés | WPRIM | ID: wpr-60698
ABSTRACT
Neurofibromatosis type 1 (NF1) is a rare genetic disease. Precapillary pulmonary hypertension (PH) with NF1 is an extremely severe complication. A 65-year-old woman was admitted in our hospital with 3-year history of gradually worsening dyspnea on exertion (New York Heart Association functional class III-IV). Considering her clinical feature and examination findings, she could be diagnosed as PH associated with NF1. She was treated with endothelin receptor antagonist. However her dyspnea was not significantly improved. This is the first Korean case of NF1 patient with PH which confirmed with right heart catheterization.
Asunto(s)

Texto completo: Disponible Índice: WPRIM (Pacífico Occidental) Asunto principal: Cateterismo Cardíaco / Neurofibromatosis 1 / Receptores de Endotelina / Neurofibromatosis / Disnea / Catéteres Cardíacos / Corazón / Concentración de Iones de Hidrógeno / Hipertensión Pulmonar Límite: Anciano / Femenino / Humanos Idioma: Inglés Revista: Kosin Medical Journal Año: 2017 Tipo del documento: Artículo

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Texto completo: Disponible Índice: WPRIM (Pacífico Occidental) Asunto principal: Cateterismo Cardíaco / Neurofibromatosis 1 / Receptores de Endotelina / Neurofibromatosis / Disnea / Catéteres Cardíacos / Corazón / Concentración de Iones de Hidrógeno / Hipertensión Pulmonar Límite: Anciano / Femenino / Humanos Idioma: Inglés Revista: Kosin Medical Journal Año: 2017 Tipo del documento: Artículo