A Case of Teratocarcinosarcoma Involving the Maxillary and Ethmoid Sinuses / 대한이비인후과학회지

ABSTRACT

Sinonasal teratocarcinosarcoma is a very unusual malignant neoplasm. This neoplasm histologically consists of an epithelial elements and one or more mesenchymal components with immature and embryonal characteristics. These tumors, which is variously termed as malignant teratoma, blastoma, teratocarcinoma, or teratocarcinosarcoma, probably comprise a group of neoplasm by their similar characteristics of histology and biology. This is a case of teratocarcinosarcoma in a 67-year-old male, involving the right maxillary sinus and ethmoid sinus with invasion of hard palate. The tumor was totally resected via total maxillectomy, and the patient was given post-operative radiotherapy. A follow-up PNS CT after 7 months of the surgery showed no recurrence of the lesion or residual tumor. Extensive tumor necrosis, rapid growth and local destruction are the prominent features of this neoplasm. The clinical presentation, pathological features and clinical course of this unusuat malignancy are discussed with a reivew of the literature.