Cerebellopontine Angle Kaposiform Hemangioendothelioma: A Case Report / 대한이비인후과학회지

ABSTRACT

Hemangioendothelioma (HE) is an uncommon vascular neoplasm, and its intracranial occurrence is extremely rare, especially in the pediatric age group. The authors report a 7-month-old male patient with kaposiform HE who presented with left-sided facial paralysis and hearing loss. Initial magnetic resonance imaging (MRI) revealed a small lesion that filled the internal auditory meatus and exhibited the neuroimaging features of a vestibular schwannoma (VS). Six months later, follow-up MRI showed markedly enlarged mass. Biopsy disclosed kaposiform HE. After vascular embolization, partial resection was performed via transmastoid approach due to massive bleeding, followed by medical treatment with steroid and interferon-alpha. The tumor nearly disappeared 6 months after medical treatment. To our knowledge, it is a first reported case of kaposiform HE mimicking a VS in the cerebellopontine angle (CPA) area. A proper diagnosis is important because its treatment differs dramatically from that of VS. So, we report this case with a literature review.