A Case of Pulmonary Arterial Hypertension Associated with Congenital Extrahepatic Portocaval Shunt
Journal of Korean Medical Science
;
: 604-608, 2014.
Artículo
en Inglés
| WPRIM
| ID: wpr-65538
ABSTRACT
Congenital extrahepatic portocaval shunt (CEPS) is a rare anomaly of the mesenteric vasculature in which the intestinal and splenic venous drainage bypasses the liver and drains directly into the inferior vena cava, the left hepatic vein or the left renal vein. This uncommon disease is frequently associated with other malformations and mainly affects females. Here we report a case of pulmonary arterial hypertension associated with CEPS (Abernethy type 1b shunt) in a 20-yr-old man who was incidentally diagnosed during evaluation of multiple nodules of the liver. The patient was treated by inhalation of iloprost (40 microg/day) with improved condition and walking test. Physicians should note that congenital portocaval shunt may cause pulmonary hypertension.
Texto completo:
Disponible
Índice:
WPRIM (Pacífico Occidental)
Asunto principal:
Arterias Torácicas
/
Vasodilatadores
/
Vena Cava Inferior
/
Imagen por Resonancia Magnética
/
Ecocardiografía Doppler
/
Tomografía Computarizada por Rayos X
/
Iloprost
/
Hipertensión Pulmonar
/
Hígado
Límite:
Humanos
/
Masculino
Idioma:
Inglés
Revista:
Journal of Korean Medical Science
Año:
2014
Tipo del documento:
Artículo
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