Dandy-Walker Syndrome with Wilms' Tumor and Congenital Cataract / 대한비뇨기과학회지

ABSTRACT

Dandy-Walker syndrome, with a Wilms' tumor, is a very rare disease. To the best of our knowledge, only 3 cases have been reported in the literature, and no case has been reported in Korea. The etiology of the two diseases combined is not known. Here we describe one case of Dandy-Walker syndrome with a Wilms' tumor and a congenital cataract in a 42-month-old female infant, with a review of the previous reports.