A Case of Neonatal Cholestasis Associated with Congenital Adrenal Hyperplasia / 대한소아소화기영양학회지
Korean Journal of Pediatric Gastroenterology and Nutrition
; : 87-90, 2005.
Article
en Ko
| WPRIM
| ID: wpr-68796
Biblioteca responsable:
WPRO
ABSTRACT
It has been suggested that cortisol deficiency may be responsible for the cholestasis. Although congenital hypopituitarism was reported as a possible cause of neonatal cholestasis, congenital adrenal hyperplasia with neonatal cholestasis is a very rare report in the literature. We experienced a case presenting with neonatal cholestasis associated with congenital adrenal hyperplasia. This case provides a clinical evidence supporting the notion that cortisol has an important physiological role in bile acid synthesis and transport.
Palabras clave
Texto completo:
1
Índice:
WPRIM
Asunto principal:
Bilis
/
Hidrocortisona
/
Colestasis
/
Hiperplasia Suprarrenal Congénita
/
Hipopituitarismo
Idioma:
Ko
Revista:
Korean Journal of Pediatric Gastroenterology and Nutrition
Año:
2005
Tipo del documento:
Article