A case of Sweet syndrome involving small bowel / 대한내과학회지

ABSTRACT

Sweet syndrome is characterized by fever and abrupt appearance of painful, erythematous plaques a dermal infiltrate of mature neutrophils. Extracutaneous manifestations often occur in Sweet syndrome, but intestinal involvement is extremely rare. We report a case of Sweet syndrome involving small bowel in a 56-year old male with fever and abdominal pain. An abdominal CT showed diffuse wall thickening in the ileal loop. He underwent explorative laparotomy and segmental resection of involved small bowel. Skin, bone marrow, and muscle biopsies were done because he had persistent fever, cutaneous plaques, pancytopenia, and swelling of lower extremities after operation. Finally, he was diagnosed as myelodysplastic syndrome combined with Sweet syndrome, which involved small bowel, skin, and muscle simultaneously. Fever, cutaneous plaques and leg swelling resolved after systemic administration of corticosteroids.