A Case of the Use of Intravenous Immunoglobulin of Treatment for HyperIgE Syndrome
Journal of the Korean Pediatric Society
;
: 1301-1304, 2001.
Artículo
en Coreano
| WPRIM
| ID: wpr-70080
ABSTRACT
Hyper-IgE syndrome is a rare congenital immune deficiency disease characterized by severe eczema, recurrent infection of the sinopulmonary tract, cold subcutaneous abscess and high serum IgE levels. It is an autosomal dominant disease with incomplete penetrance. We examined the case of a 12 month old infant with hyperIgE syndrome since neonate. The diagnosis of hyper IgE syndrome was made because he had eczema on the face and scalp, subcutaneous absecesses on both external ear canals and markedly elevated serum IgE level with a past history of frequent pulmonary disease. Topical steroid and systemic antibiotics had been unhelpful in treating the eczema and the pulmonary disease. The patient received IVIG for severe eczema and the pulmonary infection. The eczema and pulmonary infection were significantly improved and the patient was discharged after 35days of hospitalization. After 10 months of immunoglobulin therapy, symptoms and general appearance were markedly improved. IVIG can be considered as a choice in the treatment of hyper IgE syndrome.
Texto completo:
Disponible
Índice:
WPRIM (Pacífico Occidental)
Asunto principal:
Cuero Cabelludo
/
Inmunoglobulina E
/
Inmunoglobulinas
/
Inmunización Pasiva
/
Inmunoglobulinas Intravenosas
/
Penetrancia
/
Enfermedades Carenciales
/
Diagnóstico
/
Absceso
/
Conducto Auditivo Externo
Tipo de estudio:
Estudio diagnóstico
Límite:
Humanos
/
Lactante
/
Recién Nacido
Idioma:
Coreano
Revista:
Journal of the Korean Pediatric Society
Año:
2001
Tipo del documento:
Artículo
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