Oral manifestation and root canal therapy of the patient with mucopolysaccharidosis
Restorative Dentistry & Endodontics
;
: e14-2019.
Artículo
en Inglés
| WPRIM
| ID: wpr-741999
ABSTRACT
Mucopolysaccharidosis (MPS) is an inherited metabolic disorder caused by a deficiency in enzymes that participate in the degradation of glycosaminoglycans (GAGs) such as heparin sulfate and dermatan sulfate. Left untreated, patients show progressive mental and physical deterioration due to deposition of GAGs in organs. Death often occurs due to cardiac or respiratory failure before patients reach their early twenties. MPS has several oral and dental manifestations. An enlarged head, short neck, and open mouth associated with a large tongue are major characteristics of MPS patients. Dental complications can be severe, including unerupted dentition, dentigerous cyst-like follicles, malocclusions, condylar defects, and gingival hyperplasia. A 21-year-old female patient with MPS was described in this article, with special emphasis on oral manifestations and dental treatment.
Texto completo:
Disponible
Índice:
WPRIM (Pacífico Occidental)
Asunto principal:
Manifestaciones Bucales
/
Insuficiencia Respiratoria
/
Tratamiento del Conducto Radicular
/
Lengua
/
Heparina
/
Mucopolisacaridosis
/
Cavidad Pulpar
/
Dentición
/
Dermatán Sulfato
/
Hiperplasia Gingival
Límite:
Femenino
/
Humanos
Idioma:
Inglés
Revista:
Restorative Dentistry & Endodontics
Año:
2019
Tipo del documento:
Artículo
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