Pathology of C3 Glomerulopathy
Childhood Kidney Diseases
;
: 93-99, 2019.
Artículo
en Inglés
| WPRIM
| ID: wpr-785578
ABSTRACT
C3 glomerulopathy is a renal disorder involving dysregulation of alternative pathway complement activation. In most instances, a membranoproliferative pattern of glomerular injury with a prevalence of C3 deposition is observed by immunofluorescence microscopy. Dense deposit disease (DDD) and C3 glomerulonephritis (C3GN) are subclasses of C3 glomerulopathy that are distinguishable by electron microscopy. Highly electron-dense transformation of glomerular basement membrane is characteristic of DDD. C3GN should be differentiated from post-infectious glomerulonephritis and other immune complex-mediated glomerulonephritides showing C3 deposits.
Texto completo:
Disponible
Índice:
WPRIM (Pacífico Occidental)
Asunto principal:
Patología
/
Microscopía Electrónica
/
Glomerulonefritis Membranoproliferativa
/
Prevalencia
/
Activación de Complemento
/
Vía Alternativa del Complemento
/
Diclorodifenildicloroetano
/
Membrana Basal Glomerular
/
Glomerulonefritis
/
Microscopía Fluorescente
Tipo de estudio:
Estudio de prevalencia
Idioma:
Inglés
Revista:
Childhood Kidney Diseases
Año:
2019
Tipo del documento:
Artículo
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