Dental Management in a Patient with Congenital Insensitivity to Pain with Anhidrosis : A Case Report / 대한소아치과학회지
Journal of Korean Academy of Pediatric Dentistry
; (4): 416-421, 2019.
Article
en Ko
| WPRIM
| ID: wpr-787388
Biblioteca responsable:
WPRO
ABSTRACT
Congenital insensitivity to pain with anhidrosis (CIPA) is a rare, autosomal recessive disorder; affected patients are characterized by inability to feel pain and to sweat over the entire body, as well as by mental retardation. Because, in the oral examination, no specific findings on soft or hard tissue may be found except possible lesions due to self-mutilation, early recognition and diagnosis are essential for these patients. Pediatric dentists must be aware of the clinical manifestations and treatment considerations related to uncontrolled body temperature, tactile hyperesthesia and lack of pain reflex. In this case report, dental management of CIPA was suggested by presenting a 6-year follow-up of young patient.
Palabras clave
Texto completo:
1
Índice:
WPRIM
Asunto principal:
Reflejo
/
Sudor
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Temperatura Corporal
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Neuropatías Hereditarias Sensoriales y Autónomas
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Insensibilidad Congénita al Dolor
/
Estudios de Seguimiento
/
Odontólogos
/
Diagnóstico
/
Diagnóstico Bucal
/
Hiperestesia
Tipo de estudio:
Diagnostic_studies
/
Observational_studies
/
Prognostic_studies
Límite:
Humans
Idioma:
Ko
Revista:
Journal of Korean Academy of Pediatric Dentistry
Año:
2019
Tipo del documento:
Article