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A Case of Tuberous Sclerosis associated with Abdominal Aneurysm / 소아과
Korean Journal of Pediatrics ; : 583-587, 2004.
Artículo en Coreano | WPRIM | ID: wpr-7913
ABSTRACT
Tuberous sclerosis(TS) is known to be associated with multi-organ involvements, such as neurologic, renal and cardiac abnormalities. Abdominal aortic aneurysms in children and young adults are uncommon, however, some have been observed in patients with TS. We present an 8 month-old female patient with TS who developed aortic aneurysm and underwent successful surgical management. Since an aortic aneurysm is potentially lethal, patient with TS should be screened for the detection of this rare condition. Early recognition and elective surgical repair is mandatory. Because new aortic aneurysm after repair may also develop, lifelong follow-up is suggested in patients with TS complicated by aortic aneurysm.
Asunto(s)

Texto completo: Disponible Índice: WPRIM (Pacífico Occidental) Asunto principal: Aneurisma de la Aorta / Esclerosis Tuberosa / Estudios de Seguimiento / Aneurisma de la Aorta Abdominal / Aneurisma Tipo de estudio: Estudio observacional / Estudio pronóstico / Factores de riesgo Límite: Niño / Femenino / Humanos / Lactante Idioma: Coreano Revista: Korean Journal of Pediatrics Año: 2004 Tipo del documento: Artículo

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Texto completo: Disponible Índice: WPRIM (Pacífico Occidental) Asunto principal: Aneurisma de la Aorta / Esclerosis Tuberosa / Estudios de Seguimiento / Aneurisma de la Aorta Abdominal / Aneurisma Tipo de estudio: Estudio observacional / Estudio pronóstico / Factores de riesgo Límite: Niño / Femenino / Humanos / Lactante Idioma: Coreano Revista: Korean Journal of Pediatrics Año: 2004 Tipo del documento: Artículo