A Case of Myoepithelial Carcinoma Arising in the Lacrimal Gland

ABSTRACT

The vast majority of epithelial neoplasms of the lacrimal gland are pleomorphic adenomas, which comprise slightly more than 50%of epithelial tumors of this anatomic location.Other types of primary epithelial neoplasm of the lacrimal gland include adenoid cystic carcinoma, adenocarcinoma, mucoepidermoid carcinoma, and malignant mixoid tumors. Myoepitheliomas are rare tumors, most frequently reported in the salivary glands. A 61-year-old woman had painless proptosis of the right eye for 5 months. The orbit CT scan showed a lacrimal tumor involving adjacent frontoparietal bone.Histopathologically it was proved as myoepithelial carcinoma of the lacrimal gland.The patient underwent a right orbital exenteration and radiation therapy.We report this unusual case with literature review.