Malignant Fibrous Histiocytoma with Type I Neurofibromatosis
Journal of the Korean Surgical Society
;
: 167-170, 2004.
Artículo
en Coreano
| WPRIM
| ID: wpr-92214
ABSTRACT
Type I neurofibromatosis is an autosomal dominant disorder that occurs in 1 of 3, 000 births. It is characterized by multiple cutaneous neurofibromas, cafe-au-lait spots of the skin. Patients with neurofibromatosis are at increased risk of developing malignancies, particularly neural crest and other non-neural crest neoplasms. The term `malignant fibrous histiocytoma' was first introduced in 1963 to refer to a group of soft tissue tumors characterized by a storiform or cartwheel like growth pattern. Malignant fibrous histiocytomas are the most common type of soft tissue sarcoma that occurs in late adult life. Herein, our recent experienced a case of a malignant fibrous histiocytoma in a 28 year-old female with type I neurofibromatosis is reported, with a review of the literature.
Texto completo:
Disponible
Índice:
WPRIM (Pacífico Occidental)
Asunto principal:
Sarcoma
/
Piel
/
Neurofibromatosis 1
/
Neurofibromatosis
/
Manchas Café con Leche
/
Parto
/
Histiocitoma Fibroso Maligno
/
Cresta Neural
/
Neurofibroma
Límite:
Adulto
/
Femenino
/
Humanos
Idioma:
Coreano
Revista:
Journal of the Korean Surgical Society
Año:
2004
Tipo del documento:
Artículo
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