Cardiac involvement in Erdheim-Chester disease: a case report
Clin. biomed. res
;
34(4): 406-409, 2014. ilus
Article
Dans Anglais
| LILACS
| ID: biblio-834475
ABSTRACT
Erdheim-Chester disease (ECD) is a rare non-Langerhans cell histiocytosis of unknown etiology characterized by proliferation of lipid-containing foamy histiocytes affecting bones and potentially every organ. There is a wide clinical spectrum of the disease, ranging from asymptomatic bone or soft-tissue lesions to life-threatening systemic involvement. Although the initial descriptions published by Jakob Erdheim and William Chester in 1930 included a patient with right atrial infiltration on autopsy, cardiovascular involvement in ECD has only gained more recognition recently. In the present report, we describe a case with cardiac involvement, presenting with symptomatic heart failure and a cardiac mass assessed with echocardiogram and cardiac magnetic resonance imaging.
Texte intégral:
Disponible
Indice:
LILAS (Amériques)
Sujet Principal:
Échocardiographie
/
Maladie d'Erdheim-Chester
/
Défaillance cardiaque
Limites du sujet:
Femelle
/
Humains
langue:
Anglais
Texte intégral:
Clin. biomed. res
Thème du journal:
Médicament
Année:
2014
Type:
Article
Pays d'affiliation:
Brésil
Institution/Pays d'affiliation:
Hospital de Clínicas de Porto Alegre/BR
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