[Pulmonary manifestations of pediatric hyper IgE syndrome]
Medical Sciences Journal of Islamic Azad University. 2010; 20 (1): 64-67
Dans Persan
| IMEMR
| ID: emr-105440
ABSTRACT
Hyper IgE syndrome is a rare primary immune deficiency disorder characterized by pulmonary and cutaneous infection, eczema, and elevated serum IgE levels. In this article, 4 patients with hyper IgE syndrome and recurrent pulmonary infection were reported. Four girls with history of recurrent pulmonary infections were worked up and hyper IgE syndrome was diagnosed for them. All patients had recurrent pulmonary infections including pneumonia, bronchiectasis, pulmonary abscess, hydropneumothorax. Serum IgE levels were greater than 2000 Iu/ml in all cases. Microbial cultures showed staphylococcus aureas and pseudomans aeroginosa in two cases. All patients respond well to the wide spectrum intravenous antibiotics. Extra-pulmonary manifestations including purulent lymphadenitis, and skin and brain abcesses were observed. Hyper IgE syndrome causes recurrent pulmonary and extra-pulmonary infections which response fairly well to wide spectrum antibiotic therapy
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Indice:
Méditerranée orientale
Sujet Principal:
Enfant
/
Syndrome de Job
/
Maladies pulmonaires
Type d'étude:
Enquête cas-témoins / Études cas/témoins
Limites du sujet:
Femelle
/
Humains
langue:
Persan
Texte intégral:
Med. Sci. J. Islam. Azad Univ.
Année:
2010
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