Left ventricular non-compaction with associated anomalies: a rare congenital cardiomyopathy

ABSTRACT

A 22-year-old man was admitted with chief complaint of dyspnea on exertion. The patient had a history of operation 10 years ago for coarctation of the aorta. Transthoracic echocardiography showed bicuspid aortic valve, aortic regurgitation, left ventricular [LV] enlargement with ejection fraction of 45%, and a deeply trabeculated LV with deep intertrabecular recesses communicating with left ventricular cavity as demonstrated by color Doppler flow, the characteristic of the left ventricular noncompaction. Medical therapy and aortic valve replacement was performed. In the follow up, he was free of symptoms 12 months later