Prune belly syndrome with urethral hypoplasia and vesico-cutaneous fistula: a case report and review of literature

ABSTRACT

Association between Prune belly syndrome [PBS] and urethral hypoplasia is an unusual condition. It is usually fatal unless there is a communication between the fetal bladder and the amniotic sac. We report a case of PBS with urethral hypoplasia and congenital vesico-cutaneous fistula in a male neonate. Patient underwent cutaneous vesicostomy and was discharged for close follow up of his renal function and for future reconstruction