[Congenital short small intestine. a new case study]

Backgrounds: Congenital short bowel syndrome associated with malrotation and intestinal dysmotility is a rare condition. We describe a new case of this syndrome without malrotation

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Case report: Mootez is born from consanguineous parents without any familial histories. He presented with bilious vomiting at the age of ten days. The radiological exams show no sign of intestinal obstruction. Laparotomy revealed a short small bowel measuring 40 cm without malrotation. The appendice showed no anatomopathologic abnormalities. After surgery, recurrent bilious vomiting persist. He died at tow months of age from severe denutrition

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Conclusion: a precocious clinical onset and intestinal dysmotility seem to be associated with a poor prognosis. The cause of congenital short small intestine is not known. A recessive inheritance is suggested