[Desmoid tumor of shoulder-Girdle]

ABSTRACT

Desmoid tumour is an uncommon connective tissue tumour arising from musculoaponevrotic tissue characterized by spindle cell fibroblast and myofibroblast proliferation. Although considered as a benign lesion, it can be very aggressive locally, and has a high rate of local recurrences afer surgical excision. The cause is unknown and it most often encountered in young women. Abdominal localization is the most frequent site. Extra-abdominal desmoid tumors particularly located in the girdles or the most proximal part of the limbs. We report a case of a 31 year old woman with desmoid with tumour of the scapular region which was treated with wide excision, but in the following year the tumour reccured locally of the shoulder-girdle and infiltrated into the brachial plexus. Nevertheless, surgical treatment of recurrent tumors is difficult and often insufficient, compromising functional outcome. Radiotherapy has been advocated for better control tumor growth