Anesthetic considerations in patients with Dyke-Davidoff-Masson syndrome: a case report and review of literature

ABSTRACT

Dyke-Davidoff-Masson syndrome [DDMS] is a rare disorder of cerebral hemiatrophy. The clinical presentation may consist of facial asymmetry, contralateral atrophy [including the trunk and extremities], hemiparesis, speech difficulties, mental retardation and epilepsy. It involves multiple systems, especially problems of the airway, occult myopathy and seizure disorder. Anesthesia for such patients is a challenge to the anesthesiologist. We report the anesthetic care of 9 year old female child of DDMS for fractional lengthening of tendons of the forearm. Airway management, induction technique, pathophysiology of the disease, drug selection and other concerns of anesthesia have been discussed reviewing the sparse literature