Congenital hydrocephalus

ABSTRACT

Hydrocephalus results from an imbalance between the production and absorption of cerebrospinal fluid It is a common major malformation with a multifactorial aetiology. Arnold-Chiari hindbrain deformity and aqueductal stenosis are frequent underlying problems leading to congenital hydrocephalus. It is associated with deleterious long-term effects and high recurrence risk. Prompt diagnosis, adequate treatment and proper genetic counselling remain the key to successful management of this problem in children