Butterfly-shaped macular dystrophy

ABSTRACT

To report a case of butterfly-shaped macular dystrophy. A 34-year-old woman presented with metamorphopsia in both eyes from 2 years ago. Visual acuity was 9/10 in right eye and 10/10 in left eye. There was no pathologic finding on slit lamp biomicroscopy and funduscopy other than mild macular retinal pigment epithelium mottling. Visual fields and electroretinogram were normal but electrooculogram showed sub-normal results. Fluorescein angiography showed black, non-fluorescent butterfly-shaped macular structures. Butterfly-shaped macular dystrophy occurs in middle aged subjects and presents with mild visual loss and metamorphopsia. It is slowly progressive and leads to marked visual acuity reduction in older ages. Considering the paucity of clinical findings, fluorescein angiography and/ or electrophysiological tests are recommended for making a correct diagnosis