Primary extrarenal wilms' tumor in the retroperitoneum

ABSTRACT

Extrarenal Wilms' tumor is extremely rare. Approximately 54 cases have been reported in the world literature through 1993. Only eight extrarenal Wilms' tumors were enrolled in the National Wilms' Tumor Study [NWTS] between 1980 and 1986. These cases constituted a fraction of 1% of all Wilms' tumors reported to the N.W.T.S during this period. The authors report a case of retroperitoneal Wilms' tumor [Stage III] presenting as a lower abdominal mass in a previously healthy 6-year-old girl who was operated and staged according to the current N.W.T.S III criteria