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Amyotrophic lateral sclerosis: clinical analysis of 78 cases from Fortaleza (Northeastern Brazil)
Castro-Costa, Carlos M. de; Oriá, Reinaldo B; Machado-Filho, Joäo A; Franco, Maria T. G; Diniz, Débora L. O; Giffoni, Sílvio D; Santos, Terezinha J. T; Cunha, Francisco M. B. da; Bruin, Veralice S. de; Teixeira, Carlos A. C.
  • Castro-Costa, Carlos M. de; Universidade Federal do Ceará. Departamento de Fisiologia e Farmacologia. Laboratório de Neurologia Experimental.
  • Oriá, Reinaldo B; Universidade Federal do Ceará. Departamento de Fisiologia e Farmacologia. Laboratório de Neurologia Experimental.
  • Machado-Filho, Joäo A; Universidade Federal do Ceará. Departamento de Fisiologia e Farmacologia. Laboratório de Neurologia Experimental.
  • Franco, Maria T. G; Universidade Federal do Ceará. Departamento de Fisiologia e Farmacologia. Laboratório de Neurologia Experimental.
  • Diniz, Débora L. O; Universidade Federal do Ceará. Departamento de Fisiologia e Farmacologia. Laboratório de Neurologia Experimental.
  • Giffoni, Sílvio D; Universidade Federal do Ceará. Departamento de Fisiologia e Farmacologia. Laboratório de Neurologia Experimental.
  • Santos, Terezinha J. T; Universidade Federal do Ceará. Departamento de Fisiologia e Farmacologia. Laboratório de Neurologia Experimental.
  • Cunha, Francisco M. B. da; Universidade Federal do Ceará. Departamento de Fisiologia e Farmacologia. Laboratório de Neurologia Experimental.
  • Bruin, Veralice S. de; Universidade Federal do Ceará. Departamento de Fisiologia e Farmacologia. Laboratório de Neurologia Experimental.
  • Teixeira, Carlos A. C; Universidade Federal do Ceará. Departamento de Fisiologia e Farmacologia. Laboratório de Neurologia Experimental.
Arq. neuropsiquiatr ; 57(3B): 761-74, set. 1999. tab, graf
Article Dans Anglais | LILACS | ID: lil-247383
RESUMO
We report on the clinical characteristics of amyotrophic lateral sclerosis (ALS) in Fortaleza (Northeastern Brazil). For this, we analyzed retrospectively (from 1980 to 1999) 78 cases of ALS from the Service of Neutrology of the University Hospital of Fortaleza diagnosed clinically and laboratorially (EMG, muscle biopsy, myelography, blood biochemistry, muscle enzymes and cranio-cervical X-ray). The results showed that they were mostly sporadic ALS (76/78), and they were divided into definite (n=36), probable (n=20), possible (n=15) and suspected (n=7), according to the level of diagnostic certainty. They were also subdivided into juvenile (n=17), early-onset adult (n=18), age-specific (n=39) and late-onset (n=4) groups. Clinically, they presented as initals symptoms, principally, asymmetrical (30/78) and symmetrical (24/78) weakness of extremities, besides bulbar signs, fasciculations, and atrophy. Curiously, pain as first symptom occurred in an expessive fashion (17/78). The predominant initial anatomic site, in this series, was the spinal cord, and mainly affecting the arms. As to the symptom accrual from region to region, this occurs more quickly in contiguous areas, and fasciculations are predominant when bulbar region was associated.
Sujets)
Texte intégral: Disponible Indice: LILAS (Amériques) Sujet Principal: Sclérose latérale amyotrophique Type d'étude: Étude observationnelle / Facteurs de risque Limites du sujet: Adolescent / Adulte / Femelle / Humains / Mâle Pays comme sujet: Amérique du Sud / Brésil langue: Anglais Texte intégral: Arq. neuropsiquiatr Thème du journal: Neurologie / Psychiatrie Année: 1999 Type: Article

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Texte intégral: Disponible Indice: LILAS (Amériques) Sujet Principal: Sclérose latérale amyotrophique Type d'étude: Étude observationnelle / Facteurs de risque Limites du sujet: Adolescent / Adulte / Femelle / Humains / Mâle Pays comme sujet: Amérique du Sud / Brésil langue: Anglais Texte intégral: Arq. neuropsiquiatr Thème du journal: Neurologie / Psychiatrie Année: 1999 Type: Article