Achados cardíacos em 31 pacientes com síndrome de Noonan / Cardiac findings in 31 patients with Noonan's syndrome
Arq. bras. cardiol
; 75(5): 405-12, Nov. 2000.
Article
Dans Pt, En
| LILACS
| ID: lil-273496
Responsable en Bibliothèque :
BR1.1
ABSTRACT
OBJECTIVE:
To evaluate cardiac findings in 31 Noonan syndrome patients.METHODS:
Thirty-one (18 males and 13 females)patients from 26 families affected with Noonan's syndrome were evaluated from the cardiac point of view with electrocardiography and echodopplercardiography.RESULTS:
Twenty patients had some type of cardiac abnormality. The most frequent was pulmonary valve stenosis followed by hypertrophic myocardiopathy, commonly associated with valve defects. Upper deviation of the QRS axis was observed in 80 percent of these patients.CONCLUSION:
In view of the high frequency and diversity of cardiac abnormalities present in Noonan syndrome, cardiac evaluation with electrocardiography and echocardiography should be performed in all patients diagnostically suspected of having this disease
Texte intégral:
1
Indice:
LILACS
Sujet Principal:
Maladies cardiovasculaires
/
Syndrome de Noonan
Type d'étude:
Diagnostic_studies
Limites du sujet:
Adolescent
/
Adult
/
Child
/
Child, preschool
/
Female
/
Humans
/
Infant
/
Male
langue:
En
/
Pt
Texte intégral:
Arq. bras. cardiol
Thème du journal:
CARDIOLOGIA
Année:
2000
Type:
Article