Upper limb proximal form of benign monomelic amyotrophy: on purpose of 2 cases / Amiotrofia monomélica benigna forma proximal de membro superior: a propósito de 2 casos
Rev. bras. neurol
;
44(3): 13-17, jul.-set. 2008. ilus, tab
Article
Dans Anglais
| LILACS
| ID: lil-498253
ABSTRACT
Benign monomelic amyotrophy (BMA) is a rare form of motor neuron disease of unknown cause and it?s characterized by weakness and muscular atrophy restricted to an upper or lower limb, usually in the distal part, absence of upper motor neuron signs and self limited course. In this report we describe the clinical and electromyographic features of two young men with BMA in the proximal portion of the right upper limb, a location of BMA rarely described in the literature.
RESUMO
Amiotrofia Monomélica Benigna (AMB) é uma entidade rara do neurônio motor, de causa desconhecida, caracterizada por fraqueza muscular e amiotrofia restritas a 1 membro superior ou inferior, frequentemente em terço distal, sem comprometimento da via piramidal e cursoautolimitado. Descrevemos os achados clínicos e eletroneuromiográficos de 2 pacientes jovens com AMB na porção proximal do membro superior, localização raramente descrita na literatura.
Texte intégral:
Disponible
Indice:
LILAS (Amériques)
Sujet Principal:
Amyotrophie
/
Membre supérieur
/
Diagnostic différentiel
/
Maladies neuromusculaires
Type d'étude:
Etude diagnostique
Limites du sujet:
Adulte
/
Humains
/
Mâle
langue:
Anglais
Texte intégral:
Rev. bras. neurol
Thème du journal:
Neurologie
Année:
2008
Type:
Article
Pays d'affiliation:
Brésil
Institution/Pays d'affiliation:
Federal Fluminense University/BR
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