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Porokeratosis of Mibelli - literature review and a case report / Poroqueratose de Mibelli - revisao da literatura e relato de um caso
Ferreira, Flavia Regina; Santos, Leopoldo Duailibe Nogueira; Tagliarini, Fernando Augusto Nogueira Mendes; Lira, Marcia Lanzoni de Alvarenga.
  • Ferreira, Flavia Regina; Sao Paulo Federal University. Paulista Medical School.
  • Santos, Leopoldo Duailibe Nogueira; Sao Paulo Federal University. Paulista Medical School.
  • Tagliarini, Fernando Augusto Nogueira Mendes; Sao Paulo Federal University. Paulista Medical School.
  • Lira, Marcia Lanzoni de Alvarenga; Sao Paulo Federal University. Paulista Medical School.
An. bras. dermatol ; 88(6,supl.1): 179-182, Nov-Dec/2013. graf
Article Dans Anglais | LILACS | ID: lil-696801
ABSTRACT
Porokeratosis is a disorder of epidermal keratinization characterized by annular plaques with an atrophic center and hyperkeratotic edges, and includes a heterogeneous group of disorders that are mostly inherited in an autosomal dominant form. This report describes a 5 year-old female patient, with porokeratosis of Mibelli confirmed histopathologically. The rarity of this disorder, its clinical exuberance and the destructive character of the lesions, as well as the facial and mucosal involvements, unusual in this form of porokeratosis, and also its onset in early childhood motivated this report.
RESUMO
A poroqueratose é uma desordem da queratinização epidérmica caracterizada por placas anulares com centro atrófico e bordas hiperqueratóticas, e inclui um grupo heterogêneo de desordens que são na sua maioria herdadas de forma autossômica dominante. O presente caso refere-se a uma paciente feminina de 5 anos de idade, com poroqueratose de Mibelli confirmada histologicamente. A raridade desta desordem, a exuberância clínica e o caráter destrutivo das lesões, o acometimento facial e mucoso pouco usuais nesta forma de poroqueratose e o início na infância precoce motivaram este relato.
Sujets)


Texte intégral: Disponible Indice: LILAS (Amériques) Sujet Principal: Porokératose / Dermatoses faciales Limites du sujet: Enfant d'âge préscolaire / Femelle / Humains langue: Anglais Texte intégral: An. bras. dermatol Thème du journal: Dermatologie Année: 2013 Type: Article Pays d'affiliation: Brésil

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Texte intégral: Disponible Indice: LILAS (Amériques) Sujet Principal: Porokératose / Dermatoses faciales Limites du sujet: Enfant d'âge préscolaire / Femelle / Humains langue: Anglais Texte intégral: An. bras. dermatol Thème du journal: Dermatologie Année: 2013 Type: Article Pays d'affiliation: Brésil