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Poorly differentiated synovial sarcoma in the wrist - Case report
Maia, Daniela Cristina Caetano; Menezes, Carla Kellen da Silva; Bastos, Thales Costa; Ferreira, Luiz Carlos de Lima; Francesconi, Fabio.
  • Maia, Daniela Cristina Caetano; Fundação de Medicina Tropical Doutor Heitor Vieira Dourado. Manaus. BR
  • Menezes, Carla Kellen da Silva; Fundação de Medicina Tropical Doutor Heitor Vieira Dourado. Manaus. BR
  • Bastos, Thales Costa; Fundação de Medicina Tropical Doutor Heitor Vieira Dourado. Manaus. BR
  • Ferreira, Luiz Carlos de Lima; Fundação de Medicina Tropical Doutor Heitor Vieira Dourado. Manaus. BR
  • Francesconi, Fabio; Fundação de Medicina Tropical Doutor Heitor Vieira Dourado. Manaus. BR
An. bras. dermatol ; 89(5): 816-818, Sep-Oct/2014. graf
Article Dans Anglais | LILACS | ID: lil-720780
ABSTRACT
Synovial sarcomas are rare malignant tumors affecting mainly young adults, presenting as a slow growth mass located in deep soft tissues of extremities, near the joints. In this report a 34-year-old male patient, presented an ulcerovegetative lesion on the right wrist which was completely excised. Histopathology and immunohistochemistry confirmed synovial sarcomas with poorly differentiated cells. This patient presented 11 months later with ipsilateral axillary lymph node metastasis, which emphasizes the unfavorable prognosis of this synovial sarcoma variant. The indolent growth pattern of this sarcoma justifies the well circumscribed initial stages, which progressively infiltrate adjacent structures with lung metastasis (80%) and lymph node involvement (20%) and thus corroborates the importance of early diagnosis and proper treatment.
Sujets)


Texte intégral: Disponible Indice: LILAS (Amériques) Sujet Principal: Peau / Tumeurs des tissus mous / Poignet / Sarcome synovial Type d'étude: Étude pronostique / Étude de dépistage Limites du sujet: Adulte / Humains / Mâle langue: Anglais Texte intégral: An. bras. dermatol Thème du journal: Dermatologie Année: 2014 Type: Article Pays d'affiliation: Brésil Institution/Pays d'affiliation: Fundação de Medicina Tropical Doutor Heitor Vieira Dourado/BR

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Texte intégral: Disponible Indice: LILAS (Amériques) Sujet Principal: Peau / Tumeurs des tissus mous / Poignet / Sarcome synovial Type d'étude: Étude pronostique / Étude de dépistage Limites du sujet: Adulte / Humains / Mâle langue: Anglais Texte intégral: An. bras. dermatol Thème du journal: Dermatologie Année: 2014 Type: Article Pays d'affiliation: Brésil Institution/Pays d'affiliation: Fundação de Medicina Tropical Doutor Heitor Vieira Dourado/BR