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Segmental Darier's disease: a presentation of difficult diagnosis
Medeiros, Paula Mota; Alves, Natália Ribeiro de Magalhães; Trujillo, Jeniffer Muñoz; Silva, Cássia Camarinha da; Faria, Paula Carolina Pessanha de; Silva, Roberto Souto da.
  • Medeiros, Paula Mota; Universidade do Estado do Rio de Janeiro. Guarulhos. BR
  • Alves, Natália Ribeiro de Magalhães; Universidade do Estado do Rio de Janeiro. Guarulhos. BR
  • Trujillo, Jeniffer Muñoz; Universidade do Estado do Rio de Janeiro. Guarulhos. BR
  • Silva, Cássia Camarinha da; Universidade do Estado do Rio de Janeiro. Guarulhos. BR
  • Faria, Paula Carolina Pessanha de; Universidade do Estado do Rio de Janeiro. Guarulhos. BR
  • Silva, Roberto Souto da; Universidade do Estado do Rio de Janeiro. Guarulhos. BR
An. bras. dermatol ; 90(3,supl.1): 62-65, May-June 2015. ilus
Article Dans Anglais | LILACS | ID: lil-755778
ABSTRACT
Abstract

Darier's disease is a rare autosomal dominant genodermatosis. It has an estimated prevalence of 1 in 55,000 to 100,000 individuals, regardless of gender. It is characterized by multiple keratotic papules on the seborrheic areas of the trunk, scalp, forehead and flexures, and the clinical picture is worsened by heat, sun exposure, perspiration and mechanical trauma. Histopathology observed loss of epithelial adhesion and abnormal keratinization. About 10% of cases present in the localized form of the disease. We report a case of segmental Darier's Disease Type I and discuss the main characteristics of this condition.

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Sujets)


Texte intégral: Disponible Indice: LILAS (Amériques) Sujet Principal: Maladie de Darier Type d'étude: Etude diagnostique / Facteurs de risque Limites du sujet: Adulte / Femelle / Humains langue: Anglais Texte intégral: An. bras. dermatol Thème du journal: Dermatologie Année: 2015 Type: Article Pays d'affiliation: Brésil Institution/Pays d'affiliation: Universidade do Estado do Rio de Janeiro/BR

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Texte intégral: Disponible Indice: LILAS (Amériques) Sujet Principal: Maladie de Darier Type d'étude: Etude diagnostique / Facteurs de risque Limites du sujet: Adulte / Femelle / Humains langue: Anglais Texte intégral: An. bras. dermatol Thème du journal: Dermatologie Année: 2015 Type: Article Pays d'affiliation: Brésil Institution/Pays d'affiliation: Universidade do Estado do Rio de Janeiro/BR