Left ventricular noncompaction: A cardiomyopathy often mistaken.
Indian J Med Sci
;
2009 July; 63(7) 303-307
Article
Dans Anglais
| IMSEAR
| ID: sea-145424
ABSTRACT
Left ventricular noncompaction (LVNC) is a rare genetic cardiomyopathy postulated to be a defect in endomyocardial morphogenesis due to the embryonic arrest of the compaction of myocardial fibers. It could be isolated, without other structural heart defects; or associated with congenital heart defects. It is characterized by prominent ventricular myocardial trabeculations and deep intertrabecular recesses. The clinical manifestations, i.e., heart failure, arrhythmias or thromboembolism, overlap with those of other cardiac disorders. It is often misdiagnosed as restrictive or dilated cardiomyopathy. The high mortality and morbidity associated with it and familial occurrence make diagnosis important. Only 3 pediatric cases have been reported from India. We present 2 cases, that of an 11-year-old girl (familial case) with embolism (documented but rare in children) and atrial flutter (not yet reported), with mother having asymptomatic LVNC; and that of a 4-month-old girl. Both presented with heart failure. The 11-year-old child had sudden death, known to occur in LVNC.
Texte intégral:
Disponible
Indice:
IMSEAR (Asie du Sud-Est)
Sujet Principal:
Troubles du rythme cardiaque
/
Cardiomyopathie restrictive
/
Femelle
/
Humains
/
Inhibiteurs de l'enzyme de conversion de l'angiotensine
/
Captopril
/
Cardiomyopathie dilatée
/
Cardiotoniques
/
Enfant
/
Issue fatale
Type d'étude:
Etude diagnostique
langue:
Anglais
Texte intégral:
Indian J Med Sci
Année:
2009
Type:
Article
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