Pleomorphic MPNST of Breast.

ABSTRACT

Malignant peripheral nerve sheath tumors (MPNST) are a rare type of soft tissue sarcomas accounting for 5-10% of all sarcoma cases.They are a tumor of adult age group occuring in patients 20-50 years of age.Though these tumors due to their schwann cell origin may occur anywhere near a nerve trunk, breast is a rare site of its occurence.They are rare breast tumors which in association with type 1 neurofibromatosis syndrome .We report a case of pleomorphic MPNST occuring in a 32 years old female patient without any evidence of Neurofibromatosis 1 syndrome.