Syndrome of progressive ataxia and palatal myoclonus: a case report.
Article
Dans Anglais
| IMSEAR
| ID: sea-42219
ABSTRACT
A 46-year old man presented with progressive cerebellar ataxia for 5 years. Physical examination revealed palatal and tongue myoclonus, cerebellar gait, limb ataxia and spasticity of the lower extremities. The imaging studies including CT-scan and MRI of the brain revealed progressive pancerebellar atrophy and bilateral hypertrophic degeneration of inferior olives. The clinical course was slowly progressive. Various medications included anticonvulsants, benzodiazepines and antispasticity failed to abolish the abnormal palatal movement and ataxic syndrome. The syndrome of progressive ataxia and palatal myoclonus is a rare and unique neurodegenerative syndrome. The pathogenesis and treatment are still unknown.
Texte intégral:
Disponible
Indice:
IMSEAR (Asie du Sud-Est)
Sujet Principal:
Syndrome
/
Humains
/
Mâle
/
Tomodensitométrie
/
Ataxie cérébelleuse
/
Évolution de la maladie
/
Adulte
/
Myoclonie
langue:
Anglais
Année:
1999
Type:
Article
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