Combined occurrence of von Willebrand's disease and factor XIII deficiency: a case report.
Indian J Pathol Microbiol
; 2003 Apr; 46(2): 217-9
Article
de En
| IMSEAR
| ID: sea-75848
We report the case of a three year old female child with combined occurrence of von Willebrand's disease and factor XIII deficiency, an extremely rare combination. The patient presented with prolonged bleeding following cuts and wounds. Clot solubility test using 5M urea was positive. Platelet aggregation using ristocetin was reduced, which corrected on adding normal plasma. Aggregation with other agonists was normal. We discuss the clinico- hematological profile of the case. Only one such case has been reported in literature in the past to the best of our knowledge.
Texte intégral:
1
Indice:
IMSEAR
Sujet Principal:
Phénotype
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Maladies de von Willebrand
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Femelle
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Humains
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Enfant d'âge préscolaire
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Déficit en facteur XIII
langue:
En
Texte intégral:
Indian J Pathol Microbiol
Année:
2003
Type:
Article