A Case of Dissection in Marfan Syndrome with Ascending Aortic Aneurysm / 영남의대학술지
Yeungnam University Journal of Medicine
;
: 179-184, 1989.
Article
Dans Coréen
| WPRIM
| ID: wpr-108846
ABSTRACT
The Marfan syndrome is a generalized connective tissue disease involving eye, musculoskeletal system, cardiovascular system, and inherited autosomal dominant with various expression type. The cardiovascular complications such as aortic aneurysm, aortic dissection, aortic regurgitation, mitral regurgitation and aortic dissection which usually occurs in previously normal sized aorta are poor prognostic factors. However, the aortic dissection which developed in patient with Marfan syndrome and aortic aneurysm was rare. We experienced one case of dissecting aneurysm in patient diagnosed as previous aortic aneurysm, aortic regurgitation, and Marfan syndrome, receiving successful operation.
Texte intégral:
Disponible
Indice:
WPRIM (Pacifique occidental)
Sujet Principal:
Aorte
/
Anévrysme de l'aorte
/
Insuffisance aortique
/
Système cardiovasculaire
/
Maladies du tissu conjonctif
/
/
Syndrome de Marfan
/
Insuffisance mitrale
/
Appareil locomoteur
Type d'étude:
Étude pronostique
Limites du sujet:
Humains
langue:
Coréen
Texte intégral:
Yeungnam University Journal of Medicine
Année:
1989
Type:
Article
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