A Case of Neurofibromatosis with Pulsating Exophthalmos

ABSTRACT

The authors have experienced a case of neurofibromatosis with pulsating exephthlmos of the left eye of a 15 year old Korean boy. Skull P-A showed wider left orbital cavity and absence of greater and lesser wings of the left aphenoid bone. Pathologic examination was performed with biopsy which was taken fro upper lid of the left eye and conformed neurofibromatosis. The literatures relating to this disease were briafly reviewed.