A Case of Primary Ciliary Dyskinesia
Journal of Rhinology
;
: 118-122, 2017.
Article
Dans Coréen
| WPRIM
| ID: wpr-123300
ABSTRACT
Primary ciliary dyskinesia is a disease characterized by unexplained neonatal respiratory distress, otitis media, chronic sinusitis, and chronic bronchiectasis. In approximately half of cases, situs inversus totalis or other laterality defects are found. The incidence ranges from 1 in 4,000 to 1 in 40,000 live births. Early diagnosis is important and the disease is finally confirmed by electron microscopic biopsy. The treatment of primary ciliary dyskinesia is based on appropriate procedures. We present a rare case of a 20-year-old male with bronchiectasis, chronic otitis media and chronic sinusitis.
Texte intégral:
Disponible
Indice:
WPRIM (Pacifique occidental)
Sujet Principal:
Otite moyenne
/
Sinusite
/
Situs inversus
/
Biopsie
/
Dilatation des bronches
/
Syndrome de Kartagener
/
Incidence
/
Diagnostic précoce
/
Naissance vivante
Type d'étude:
Etude diagnostique
/
Etude d'incidence
/
Étude pronostique
/
Étude de dépistage
Limites du sujet:
Humains
/
Mâle
langue:
Coréen
Texte intégral:
Journal of Rhinology
Année:
2017
Type:
Article
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