A Cases of Adult Onset Still's Disease with Hemolytic Anemia
Journal of Rheumatic Diseases
;
: 104-107, 2012.
Article
Dans Coréen
| WPRIM
| ID: wpr-135253
ABSTRACT
Adult onset Still's disease (AOSD) is a systemic inflammatory disorder of unknown etiology. AOSD is characterized by fever, arthralgia, salmon-colored skin rash, hepatosplenomegaly and its laboratory abnormalities include leukocytosis, elevated liver enzyme, negative autoantibody, and hyperferritinemia. The clinical course varied and severe complicated conditions, such as hemophagocytic syndrome, and disseminated intravascular coagulation, occurred occasionally. Such a complication is accompanied with hemolytic anemia and lead to be a fatal course. We report the first case of AOSD with hemolytic anemia, which improved with high dose steroid therapy.
Texte intégral:
Disponible
Indice:
WPRIM (Pacifique occidental)
Sujet Principal:
Maladie de Still débutant à l'âge adulte
/
Arthralgie
/
Coagulation intravasculaire disséminée
/
Lymphohistiocytose hémophagocytaire
/
Exanthème
/
Fièvre
/
Anémie hémolytique
/
Hyperleucocytose
/
Foie
Limites du sujet:
Adulte
/
Humains
langue:
Coréen
Texte intégral:
Journal of Rheumatic Diseases
Année:
2012
Type:
Article
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